A Developmental Complex Including Supravalvular Stenosis of the Aorta and Pulmonary Trunk
A developmental complex is described characterized by (1) supravalvular stenosis of the aorta and pulmonary trunk, (2) dysplasia of valves and (3) stenosis of ostia of coronary arteries and branches of the aortic arch. From the four cases described, it is evident that not all of the features of the complex need be present in a given case and, when present, some lesions are not of functional significance. The variations underly the potential for differences in the hemodynamic states of affected subjects.
- Peripheral pulmonary arterial stenosis
- Congenital coronary ostial stenosis
- Multiple valvular disease
- Aortic arch syndrome
- © 1974 American Heart Association, Inc.