Cor Triloculare Biatriatum
Survival to Adult Life
The case of a 41-year-old woman with congenital pulmonary stenosis and single ventricle is reported. This is the fifteenth instance recorded of survival to adult life of a patient with cor triloculare biatriatum. Increased pulmonary resistance may be a reason for her comparative longevity, and the significance of prominent bronchopulmonary anastomoses has been discussed. This patient's course demonstrates the hazards of phlebotomy in congenital heart disease and secondary polycythemia. The mechanism for this adverse effect is not understood and warrants further study. Although others have discussed the problem informally, this appears to be the first documented report of the precipitation of multiple cerebral thromboses following phlebotomies.
- © 1961 American Heart Association, Inc.