At birth, this patient was diagnosed with inoperable complex congenital cyanotic heart disease. With her short life expectancy, she was sent to Symi Island, Greece, to live with her grandparents. Surprisingly, she grew up without significant limitations and returned to the United States at age 10 years. She is now 73 years old and has had 3 children. Transthoracic echocardiogram (Figure) illustrates a univentricular heart with double-inlet left ventricle. The left atrium and right atrium empty into one ventricle. Severe subvalvular pulmonic stenosis and levo-transposition of the great vessels are present. She has never had cardiac surgery. We believe she is the oldest living patient with an uncorrected single ventricle. Her longevity is partly due to subvalvular pulmonic stenosis, which has protected her pulmonary circulation from volume overload. She is mildly hypoxic with room air oxygen saturation of 84%, but overall, continues to do well.
The editor of Images in Cardiovascular Medicine is Hugh A. McAllister, Jr, MD, Chief, Department of Pathology, St Luke’s Episcopal Hospital and Texas Heart Institute, and Clinical Professor of Pathology, University of Texas Medical School and Baylor College of Medicine.
Circulation encourages readers to submit cardiovascular images to the Circulation Editorial Office, St Luke’s Episcopal Hospital/Texas Heart Institute, 6720 Bertner Ave, MC1-267, Houston, TX 77030.