Rare Cause of Cardiomyopathy
A 62-year-old man with scleredema of Buschke was referred to the cardiology clinic because of an abnormal ECG. He had no cardiac symptoms, and the cardiovascular examination was unremarkable. The echocardiogram showed a dilated, nonhypertrophied left ventricle with no regional wall motion abnormalities and an estimated ejection fraction of 15%. The right ventricle was normal in size and systolic function. Coronary angiography showed significant proximal disease in the right coronary artery and distal circumflex artery. The left main stem and left anterior descending arteries were angiographically normal. Myocardial biopsies taken from the right ventricle showed histology typical of scleredema of Bushke, which has not previously been shown antemortem in the heart (Figure⇓).
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